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单词 adrenoleukodystrophy
释义

adrenoleukodystrophy

英汉-汉英词典
肾上腺脑白质营养不良
词组 | 习惯用语
adrenoleukodystrophy n. 肾上腺脑白质营养不良

网络短语:
Adrenoleukodystrophy 肾上腺脑白质失养症; 肾上腺脑白质营养不良; ALD蛋白; 肾上皮脑白质失养;
neanatal adrenoleukodystrophy 肾上腺脑白质营养不良
neonatal adrenoleukodystrophy 不良;新生儿肾上腺脑白质营养不良
X-linked adrenoleukodystrophy 脑白质营养不良;白质营养不良;肾上腺脑白质营养不良
ALD adrenoleukodystrophy 肾上腺脑白质营养不良
adrenoleukodystrophy protein 肾上腺脑白质营养不良蛋白
adrenoleukodystrophy fatty acids gas 肾上腺皮质营养不良
英语例句库
  1. Adrenoleukodystrophy (ALD) is a degenerative disorder of myelin, a complex fatty neural tissue that insulates many nerves of the central and peripheral nervous systems.
    什么是'肾上腺脑白质营养不良-退行性疾病的神经髓鞘覆盖'?
  2. And the diagnoses of several famous hospitals all showed that both of these two boys suffered the disease named Adrenoleukodystrophy(ALD/AMN) which is a rare cranial nerve disease in the world.
    经过各大医院医生的综合仔细诊断显示,二个儿子同时患上了世界上罕见的脑神经疾病——肾上腺脑白质退化症。

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中文百科

肾上腺脑白质失养症

肾上腺脑白质失养症(ALD, Adrenoleukodystrophy),是一种脑内去髓鞘化白质化的遗传病,其通常分作儿童型脑白质化、青少年大脑型、肾上腺脊髓性神经病变型及女性异型合子病征基因型。患者细胞的过氧化体在代谢较长的链脂肪酸时产生异常,尤其是C24、C26长链脂肪酸会异常堆积在大脑的白质和肾上腺的皮质内,进而侵蚀患者脑神经系统的髓鞘质,造成患者的髓鞘脱失,脑部的神经细胞因此就会被摧毁,进而妨碍神经的传导。

英语百科

Adrenoleukodystrophy 肾上腺脑白质失养症

Adrenoleukodystrophy (/-ˌlu-k-ˈdis-trə-f/; also known as X-linked adrenoleukodystrophy, ALD, X-ALD, adrenomyeloneuropathy, AMN, Siemerling–Creutzfeldt disease or bronze Schilder disease) is a disease that is linked on the X chromosome. It is a result of fatty acid digestive enzymes not breaking up the fats. These fats build up in the brain. They damage the myelin that surrounds nerves. This can cause seizures and hyperactivity. It can also cause problems with speaking, listening and understanding verbal instructions.

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更新时间:2025/6/21 16:22:22